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Invasive ductal carcinoma of the mammary like glands of vulva-with sentinel lymph node identification

Cumhuriyet Medical Journal(2013)

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摘要
Abstract Breast like carcinomas of the vulva was thought to be originated from ectopic breast tissue or metastasis from breast. It is now accepted that, as mammary-like glands are present in the vulva, any pathology that is found in the breast can be seen at these glands. Adenocarcinoma of the vulva is rare and the breast-like adenocarcinomas are presented as case reports in the literature. We present a primary breast-like carcinoma of the vulva in a 70 year old patient, who had complaint of vulvar mass and bleeding from it. The incisional biopsy was reported as vulvar adenocarcinoma. The intraoperative diagnosis of sentinel lymph node was adenocarcinoma metastasis and hemivulvectomy together with bilateral inguinal lymphadenectomy was carried out. Adenocarcinomas of vulva are very rare and breast like carcinoma must be kept in mind in these cases, as the prognosis and treatment is similar to primary breast carcinomas. Keywords: Vulva, vulvar neoplasms, breast, carcinoma, ductal Ozet Vulvanin meme benzeri karsinomlarinin ektopik meme dokusundan kaynaklandigi veya meme karsinomu metastazi oldugu dusunulmustur. Ancak, su anda, vulvada meme-benzeri bezler oldugu icin, memede gorulen herhangi bir patolojinin bu bezlerde gorulebilecegi kabul edilmektedir. Vulvanin adenokarsinomu nadir olup, meme-benzeri adenokarsinomlari literaturde olgu sunumlari seklinde yer almaktadir. Vulvar kitle ve kanama sikayetiyle basvuran 70 yasindaki hastada tanimladigimiz vulvanin primer meme benzeri karsinomu olgusunu sunuyoruz. Insizyonel biyopsi vulvar adenokarsinom olarak raporlandi. Intraoperatif sentinal lenf dugumu incelemesi adenokarsinom metastazi olan hastaya hemivulvektomi ve bilateral inguinal lenfadenektomi uygulandi. Vulvanin adenokarsinomlari nadir olup, prognoz ve tedavi primer meme kanseri ile benzerlik gosterdigi icin bu olgularda meme benzeri karsinom akilda tutulmalidir. Anahtar sozcukler: Vulva, vulvar tumorler, meme, karsinoma, duktal
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