Primary cutaneous CD8+ T-cell lymphoma masquerading as acral vascular syndrome.

Acral vascular syndromes (AVS) require thorough testing as, they can reveal varied underlying conditions, including immunological and haematological disorders or neoplasia (1). We report here the first case of primary cutaneous CD8(+) T-cell lymphoma (CTCL) presenting with ulcerated infiltrated patches exclusively located on acral areas including fingers, toes, ears and nose. This case which evolved over 4 years, raises challenging questions as to how it should be classified and as to whether it may impact our current diagnostic approach to AVS.