Provisional diagnosis of early-onset Behçet disease in a 3-year-old girl.

Diagnosis of Behçet disease (BD), a chronic multisystemic vasculitis of unknown origin, can be made relying on the combination of recurrent oral ulcers plus 2 of the following signs: recurrent genital ulcerations, uveal or retinal disease, peculiar skin lesions (erythema nodosum and papulopustular/acneiform nodules), or a positive pathergy test. 1 Rigante D. The fresco of autoinflammatory diseases from the pediatric perspective. Autoimmun Rev. 2012; 11: 348 Crossref PubMed Scopus (55) Google Scholar Cases of BD have been reported worldwide, but the pediatric identification of BD is infrequent and demanding. 2 Al Mosawi Z.S. Madan W. Fareed E. Pediatric-onset Behçet disease in Bahrain: report of nine cases and literature review. Arch Iran Med. 2012; 15: 485 PubMed Google Scholar