Localized sclerosing cholangitis in the intrapancreatic bile duct. Report of a case.

A case of primary sclerosing cholangitis (PSC) localized in an isolated segment of the intrapancreatic bile duct was successfully treated by a pancreatico-duodenectomy. Although a progressively larger number of patients with PSC have recently been reported, there have been no other reports of a patient with this disease confined to the very distal part of the common bile duct. Since it is difficult to differentiate this rare disease from malignancy, surgical treatment as for a malignancy is sometimes required.