传统中药治疗特发性肺纤维化的研究进展

Chinese Journal of Clinicians(Electronic Edition)(2010)

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Abstract
特发性肺纤维化(idiopathic pulmonary fibrosis,IPF)是指病因不明并以普通型间质性肺炎(usual interstitial pneumonia,UIP)为特征性病理改变的慢性炎症性间质性肺疾病.肺纤维化(pulmonary fibrosis,PF)是多种弥漫性间质性肺疾病(interstitial lung disease,ILD)发展到晚期的共同的病理改变和结局,病理上主要表现为早期的弥漫性肺泡炎和晚期大量成纤维细胞的病理性增生以及基质胶原的进行性积聚,是对损伤的过度修复,最终发展为弥漫性肺间质纤维化和蜂窝肺.I
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