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先天性双手“镜相”多指畸形1例

Medical Journal of National Defending Forces in Northwest China(2009)

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Abstract
患者,男性,1.5岁,哈萨克族,出生时双手小指近端指间关节内侧见黄豆大小、质地软、有弹性的小结节影,并有一狭颈与手指部软组织相连,以后随年龄增长并不断增大而来院就诊.X线检查:双手小指内侧近节指骨头部见直径约1.0 cm的软组织影,有一狭颈与指骨周围软组织相连,其内密度均匀,未见骨骼,余手诸骨骨质及周围软组织未见异常.诊断:双手多指畸形.手术切除所见:该软组织内无骨骼、软骨及肌腱.
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