46. Human primary chondrocytes, a relevant model of mucopolysaccharidosis IVA, internalize N-acetylgalactosamine-6-sulfate sulfatase into lysosomes, resulting in clearance of keratan sulfate
Molecular Genetics and Metabolism(2009)
关键词
human primary chondrocytes,mucopolysaccharidosis iva,keratan n-acetylgalactosamine-6-sulfate,lysosomes
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