Congenital pulmonary atresia with intact ventricular septum clinicopathologic correlation of two anatomic types

A clinical and pathologic study was made in 20 cases of pulmonary atresia with intact ventricular septum proved at necropsy. The hearts usually could be divided readily into two groups, namely, those with a small or tiny right ventricle (Type 1) and those with a right ventricle of normal size or larger (Type 2); 13 hearts were of Type 1, and 7 were of Type 2.