The Pediatric Renal Clear Cell “Sugar” Tumor: Pseudo-alveolar Structure Mimicking Clear Cell Renal Carcinoma

The primary extrapulmonary sugar tumor (PEST) is rare. Up to now, only 16 cases of PEST have been reported, including 5 pediatric cases. We report a renal benign PEST in a 16-year-old boy, which is the first such case to be reported in the pediatric kidney. The tumor was composed of clear and eosinophilic epithelioid cells, growing with nest and pseudoalveolar structure, which can be confused with renal clear cell carcinoma. The tumor cells were positive for melanocytic and negative for epithelial markers. The tumor was enucleated, and the patient was well without recurrence 21 months after surgery. UROLOGY 77: 205-207, 2011. (C) 2011 Elsevier Inc.