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Primary Pulmonary Hypertension

Pulmonary Arterial Hypertension and Interstitial Lung Diseases(2009)

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摘要
Primary pulmonary hypertension (PPH) is a disease of the pulmonary vasculature defined by an increase in pulmonary vascular resistance (PVR) that eventually leads to heart failure and premature death. Fifty years after the original antemortem description of PPH (1), the cause remains unknown, and no cure is available.
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